Involved in mitochondrion organization. Acts upstream of with a positive effect on determination of adult lifespan. Located in mitochondrion and striated muscle dense body. Expressed in intestine and ventral nerve cord. Human ortholog(s) of this gene implicated in isolated mitochondrial myopathy and neurodegenerative disease (multiple). Is an ortholog of human CHCHD10 (coiled-coil-helix-coiled-coil-helix domain containing 10).
Map position created from combination of previous interpolated map position (based on known location of sequence) and allele information. Therefore this is not a genetic map position based on recombination frequencies or genetic experiments. This was done on advice of the CGC.